UNIVERSITAS AIRLANGGA



Detail Article

Jurnal Oftalmologi Indonesia

ISSN 1693-2587

Vol. 7 / No. 5 / Published : 2011-06

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Original Article :

Crouzon syndrome

Author :

  1. Dewi Rosarina*1
  2. Hendrian D. Soebagdjo*2
  1. Department of Ophthalmology, Faculty of Medicine Airlangga University/Dr. Soetomo General Hospital, Surabaya

Abstract :

To report a case of patient with Crouzon syndrome. A case report, a 5 years old boy came to outpatient clinic with proptosis on his both eyes since birth . His parents also said the palate was deep and narrower than normal. Examination of the right eye releaved: visual acuity was 6/12 , intraocular pressure was normal palpation, anterior segment was proptosis, the other was within normal limit. Examination of the left eye revealed: visual acuity was 6/6, intraocular pressure was normal palpation, anteriorsegment was proptosis, the other was within normal limit. Ocular motility showed mild restriction on both eyes. There was no strabismus. Examination of the fundus revealed: Fundal Reflex was positive, sharp margin optic disc with normal colour, no retinal haemorrhage, no exudate, macular reflex was positive. CT-scan examination revealed internum hydrocephalus, and there was no retrobulber mass. MRI examination revealed bilaterally exophthalmos, relatively ventriculomegaly caused by skull anomaly (oxycephaly). Proptosis in this patient was caused by shallow orbits in crouzon syndromes. Radiological examination results a features showed patients with Crouzon syndrome. Crouzon syndrome is an example of such a syndrome that is associated with premature synostosis of the suturesof the skull, exophthalmos, head, orbit and jaw deformities.

Keyword :

Crouzon syndrome, proptosis, jaw deformities, hydrocephalus, oxycephaly,


References :

Maloth et al,(2010) Diagnosis of Crouzon’s syndrome: a case report Hongkong : Hong Kong Dent J

Arathi R, Sagtani A, Baliga M,(2007) Crouzon’s syndrome: a case report India : J Indian Soc Pedod Prevent Dent

Holds et al,(2009) Congenital Orbital Anomalies on Orbit, Eyelids, and Lacrimal System San Fransisco : American Academy of Opthalmology

Dorivaldo Lopes da Silva et al,(2008) Crouzon’s Syndrome: Literature Review Brazil : Journal of Otolaryngology





Archive Article

Cover Media Content

Volume : 7 / No. : 5 / Pub. : 2011-06
  1. Limbal Dermoid And Pre-auricular Tag In A 12 Years Old Girl
  2. Vitrectomy And Silicone Oil Tamponade In The Management Of Retinal Detachment In Marfan Syndrome Patient
  3. Crouzon Syndrome
  4. Histopathologic Profile Grading Of Haematoxylene Eosin On Retinoblastoma Stadium
  5. Decrease Of Corneal Sensitivity In Patients With Diabetes Mellitus Type Ii
  6. Glaucoma Caused Blindness With Its Characteristic In Cipto Mangunkusumo Hospital
  7. Visual Field Abnormality And Quality Of Life Of Patient With Primary Open Angle Glaucoma
  8. The Role Of Ascorbic Acid On Endothelial Cell Damage In Phacoemulsification
  9. The Risk Factors Of Human Papilloma Virus 18 On The Recurrences Of Pterygium
  10. Crouzon Syndrome

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